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Spotlight On

Hypercortisolism in Resistant Hypertension

An underrecognized driver of resistant hypertension, increasingly documented in cardiology patients — distinct from the classic Cushing's syndrome phenotype

Prevalence

10–15 to ~40–49 cases per million person-years 1

Classic Cushing's syndrome (overt form)

27.3% (MOMENTUM, 297/1,086 patients)2,3

Non-classic hypercortisolism — resistant hypertension

23.8% (CATALYST, 252/1,057 patients)4

Non-classic hypercortisolism — difficult-to-control T2D

Age of Onset

ageofonset adult

Typically during the fourth to fifth decades of life.

ICD-10

E24.9

(Cushing's syndrome, unspecified) — no dedicated code exists for non-classic/mild autonomous cortisol secretion.

There is no established general-population prevalence for non-classic hypercortisolism — it has only been measured within at-risk clinical populations, which is itself part of the story: this isn't found by general screening, it's found by screening the patients already in front of you who aren't responding to standard treatment.

5 Facts you should know

FACT

1

Non-classic, mild hypercortisolism is increasingly recognized in common cardiometabolic conditions and looks nothing like the overt phenotype of classic Cushing's syndrome (moon face, striae, buffalo hump), which means it can be missed using classic diagnostic criteria alone

FACT

2

Patients with hypercortisolism-driven hypertension often present first to cardiology for resistant or difficult-to-control blood pressure, without any visible Cushingoid features

FACT

3

MOMENTUM, a large U.S. study of 1,086 adults with resistant hypertension, found endogenous hypercortisolism in 27.3% of patients using the 1-mg overnight dexamethasone suppression test (DST)

FACT

4

Excess cortisol raises blood pressure through several concurrent mechanisms, including mineralocorticoid receptor activation, renal sodium retention, upregulation of angiotensin II type 1 receptors, and impaired nitric oxide signaling

FACT

5

The 1-mg overnight DST — one bedtime dose of dexamethasone, one morning cortisol level — is the standard first-step screening test and can be ordered without a specialist referral

Hypercortisolism is also known as...

Hypercortisolism is also known as:

  • Non-classic hypercortisolism

  • Mild autonomous cortisol secretion (MACS)

  • Subclinical Cushing's

What’s your Rare IQ?

In your view, how much of a factor does hypercortisolism play in resistant hypertension?

Common signs & symptoms

Resistant hypertension

Blood pressure uncontrolled despite three or more antihypertensive agents, including a diuretic

No visible Cushingoid features

non-classic hypercortisolism frequently presents without moon face, striae, or buffalo hump

Comorbid difficult-to-control glucose

Prevalence is elevated in patients managing both resistant hypertension and difficult-to-control type 2 diabetes

Screening & Diagnosis

1-mg overnight DST

one bedtime dexamethasone dose, one morning cortisol level — you can order this directly, no referral needed to start

Positive threshold

 Post-DST cortisol above 1.8 µg/dL

A positive result is a screen, not a diagnosis

it's your referral trigger, not a treatment decision point

Management Approach

A positive screen is a clear, concrete reason to refer to endocrinology for confirmatory testing

You are not expected to interpret borderline results or manage etiology — that's the referral's purpose

Continue managing hypertension and glucose control in parallel while the referral is pending

Clinical trials

TitleDescriptionPhasesStatusInterventionsMore Information
Study of the Prevalence of Endogenous Hypercortisolism in Patients With Resistant Hypertension (MOMENTUM)This is a non-interventional study to assess the prevalence of endogenous hypercortisolism (eHC) in patients with resistant hypertension (rHTN) and will enroll approximately 1000 patients at approximately 45 sites in the United States (US).

Each patient will have an initial visit for screening. Aft...
N/ACompletedMore Info
Study to Determine the Prevalence of Hypercortisolism in Patients With Type 2 Diabetes and Treatment With Korlym® (Mifepristone) (CATALYST)This is a Phase 4 study with 2 parts: Part 1 (Prevalence Phase) is non-interventional and will assess the prevalence of hypercortisolism in a population with difficult to control type 2 diabetes (T2D) (hemoglobin A1c ≥7.5%) despite receiving standard-of-care therapies. Part 2 (Treatment Phase) is a...Phase 4CompletedDrug: Mifepristone 300 MG [Korlym]
Drug: Placebo for mifepristone
More Info
A Study to Evaluate the Safety and PK of CRN04894 for the Treatment of Cushing's SyndromeA Phase 1b/2a, first-in-disease, open-label, multiple-ascending dose exploratory study to evaluate safety, tolerability, pharmacokinetics (PK), and pharmacodynamic biomarker responses associated with CRN04894 (an adrenocorticotropic hormone \[ACTH\] receptor antagonist) in participants with ACTH-dep...Phase 1, Phase 2RecruitingDrug: atumelnantMore Info
A Block-and-Replace Therapy With Osilodrostat and Concomitant Glucocorticoid ReplacementThe major goal of this study is to determine the incidence of adrenal insufficiency in patients with endogenous Cushing syndrome receiving osilodrostat treatment combined with a replacement of glucocorticoid (block-and-replace approach).

The investigators are also evaluating new biomarker steroids...
RecruitingDrug: OsilodrostatMore Info
Combination Osilodrostat and Cabergoline in Cushing's DiseaseCushing disease remains a challenging endocrine disorder in which persistent or recurrent hypercortisolism often requires medical therapy after surgery or when surgery is not feasible. Combination medical therapy has emerged as a rational strategy to improve biochemical control through complementary...Phase 4Enrolling by invitationDrug: osilodrostat
Drug: osilodrostat and cabergoline
More Info
Isturisa Treatment in Mild Autonomous Cortisol Secretion( MACS)To characterize the impact of Isturisa on clinical features and comorbidities associated with MACS. The investigators hypothesize that patients treated with Isturisa will exhibit significantly better metabolic indicators (such as fasting glucose, HbA1c, and lipid profile), blood pressure, weight, bo...Phase 4RecruitingDrug: Osilodrostat (Isturisa)More Info
Extension Study to Evaluate the Safety of Long-Term Use of Relacorilant in Patients With Cushing SyndromeThis is an open-label extension study to evaluate the long-term safety of relacorilant in patients with endogenous Cushing syndrome who successfully completed participation in a Corcept-sponsored study of relacorilant and may benefit from continuing treatment.Phase 2ActiveDrug: relacorilantMore Info
Effect of Metyrapone on Cardiovascular Risk Factors in Patients With Adrenal Incidentalomas and Cushing's SyndromeDrug interventional, controlled, randomized open-label, parallel-group, multicenter study in patients with bilateral adrenal incidentalomas associated with subclinical Cushing's syndromePhase 4RecruitingDrug: Metarapone
Drug: Standardized antihypertensive therapy
More Info
Metyrapone for Mild Autonomous Cortisol Secretion (MACS)The purpose of this study is to find out whether the study drug, metyrapone, is safe and effective in treating participants with Mild Autonomous Cortisol Secretion (MACS).Phase 2ActiveDrug: MetyraponeMore Info
Desmopressin Stimulation Test Performance in ACTH-Dependent Cushing SyndromeBackground:

Cushing syndrome (CS) is a set of diseases that develop when the body produces too much adrenocorticotropic hormone (ACTH). ACTH stimulates the production of a hormone called cortisol. Excess cortisol can cause serious issues, such as diabetes, high blood pressure, weight gain, and mood...
Phase 2RecruitingDrug: Desmopressin
Drug: Dexamethasone
More Info
Diagnostic Value of CXCR4-targeted PET/CT in ACTH-dependent and Independent Cushing's SyndromeIn previous clinical practice, 68Ga-Pentixafor PET/CT has demonstrated promising diagnostic utility in various neuroendocrine tumors by targeting CXCR4, a chemokine receptor overexpressed in several ACTH-secreting neoplasms. Building on this, and leveraging the Nuclear Medicine expertise at Peking U...Phase 1, Phase 2RecruitingDrug: 68Ga-PentixaforMore Info
Long-Term Follow-Up of Survivors of Pediatric Cushing DiseaseBackground:

The pituitary gland produces hormones. A tumor in this gland can cause it to produce too much of the hormone cortisol. Too much cortisol in the body causes Cushing disease. This disease causes many problems. Some of these problems might persist after the disease is cured.

Objective:

T...
RecruitingMore Info